Creutzfeldt-Jakob Syndrome
《英文msh詞典》Creutzfeldt-Jakob Syndrome
[主題詞] Creutzfeldt-Jakob Syndrome
[同義詞] CJD Variant (V-CJD)
[同義詞] New Variant Creutzfeldt-Jakob Disease
[同義詞] Spongiform Encephalopathy,Subacute
[入口詞] CJD
[入口詞] CJD (Creutzfeldt-Jakob Disease)
[入口詞] Creutzfeldt-Jakob Disease
[入口詞] Creutzfeldt-Jakob Disease,Familial
[入口詞] Creutzfeldt-Jakob Disease,New Variant
[入口詞] Familial Creutzfeldt-Jakob Disease
[入口詞] Jakob-Creutzfeldt Disease
[入口詞] Jakob-Creutzfeldt Syndrome
[入口詞] V-CJD (Variant-Creutzfeldt-Jakob Disease)
[入口詞] CJD (Creutzfeldt Jakob Disease)
[入口詞] CJD Variant (V CJD)
[入口詞] CJD Variants (V-CJD)
[入口詞] CJDs (Creutzfeldt-Jakob Disease)
[入口詞] Creutzfeldt Jakob Disease
[入口詞] Creutzfeldt Jakob Disease,Familial
[入口詞] Creutzfeldt Jakob Disease,New Variant
[入口詞] Creutzfeldt Jakob Syndrome
[入口詞] Creutzfeldt-Jakob Diseases,Familial
[入口詞] Disease,Creutzfeldt-Jakob
[入口詞] Disease,Familial Creutzfeldt-Jakob
[入口詞] Disease,Jakob-Creutzfeldt
[入口詞] Encephalopathies,Subacute Spongiform
[入口詞] Encephalopathy,Subacute Spongiform
[入口詞] Familial Creutzfeldt Jakob Disease
[入口詞] Familial Creutzfeldt-Jakob Diseases
[入口詞] Jakob Creutzfeldt Disease
[入口詞] Jakob Creutzfeldt Syndrome
[入口詞] New Variant Creutzfeldt Jakob Disease
[入口詞] Spongiform Encephalopathies,Subacute
[入口詞] Subacute Spongiform Encephalopathies
[入口詞] Subacute Spongiform Encephalopathy
[入口詞] Syndrome,Creutzfeldt-Jakob
[入口詞] Syndrome,Jakob-Creutzfeldt
[入口詞] Variant,CJD (V-CJD)
[入口詞] Variants,CJD (V-CJD)
[中文釋義] 克-亞綜合征
[英文釋義] A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances,personality changes,ATAXIA; APHASIA,visual loss,weakness,muscle atrophy,MYOCLONUS,progressive dementia,and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY,BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med,1998 Dec 31;339(27))